POLYCYSTIC OVARIES AND GLUCOSETOLERANCE IN HEPATIC GLYCOGEN STORAGE DISEASE
نویسندگان
چکیده
منابع مشابه
The dietary management of hepatic glycogen storage disease.
The dietary management of hepatic glycogen storage disease (GSD) is based on an understanding of the primary biochemical abnormalities. Plasma glucose levels are maintained by the release of glucose from the liver. The glucose is formed either by the breakdown of glycogen or it is synthesized from substrates such as fructose, galactose, glycerol or amino acids. The final common step in all thes...
متن کاملENVIRONMENTAL FACTORS AND POLYCYSTIC OVARIES
This study was designed to investigate the effect of environmental factors on the appearance of polycystic ovaries (PCO) during the first two decades of life. Ninety-four female-female twins who underwent a transabdominal ultrasound at the Royal Hospital for Women were sent a questionnaire asking about their birth details, feeding history as a baby, childhood illnesses and vaccination as w...
متن کاملPompe's Glycogen Storage Disease
The clinical spectrum is continuous and broad and three major forms are recognised: infantile, juvenile and adult-onset. [1] In the infantile form, accumulation of glycogen in cardiac muscle leads to cardiac failure. Accumulation may also occur in the liver, which results in hepatomegaly and elevation of hepatic enzymes. Glycogen accumulation in muscle and peripheral nerves causes hypotonia and...
متن کاملPompe's Glycogen Storage Disease
The clinical spectrum is continuous and broad and three major forms are recognised: infantile, juvenile and adult-onset. [1] In the infantile form, accumulation of glycogen in cardiac muscle leads to cardiac failure. Accumulation may also occur in the liver, which results in hepatomegaly and elevation of hepatic enzymes. Glycogen accumulation in muscle and peripheral nerves causes hypotonia and...
متن کامل[Glycogen storage disease].
The glycogen storage diseases (GSD) or glycogenoses are a heterogenous group of inborn errors of carbohydrate metabolism that lead to abnormal concentrations or structure of glycogen. Several well defined disorders of glycogen metabolism, have been described based on the identified enzymatic defects or sometimes the distinctive features(l). We wish to report our experience with one such case of...
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ژورنال
عنوان ژورنال: Pediatric Research
سال: 1993
ISSN: 0031-3998,1530-0447
DOI: 10.1203/00006450-199305001-00063